Pulmonary Capillary Hemangiomatosis With Severe Pulmonary Hypertension
Open Access
- 1 January 2003
- journal article
- case report
- Published by Japanese Circulation Society in Circulation Journal
- Vol. 67 (9), 793-795
- https://doi.org/10.1253/circj.67.793
Abstract
Pulmonary capillary hemangiomatosis (PCH) is a rare idiopathic lung disorder that occurs in young patients and leads to pulmonary hypertension (PH). It is difficult to diagnosis in the early stage and is often mistaken for primary PH; in almost all cases of PCH, the correct diagnosis is not made until autopsy. In the present case of PCH, the patient had severe pulmonary hypertension and died of respiratory failure. Pathologically, PCH is characterized by proliferation of benign thin-walled capillary sized blood vessels in the lung parenchyma. (Circ J 2003; 67: 793 - 795)Keywords
This publication has 10 references indexed in Scilit:
- An autopsy case of pulmonary capillary hemangiomatosis without evidence of pulmonary hypertensionVirchows Archiv, 2001
- Pulmonary Capillary Hemangiomatosis–Like FociAmerican Journal of Clinical Pathology, 2000
- Pulmonary veno-occlusive diseaseCurrent Opinion in Pulmonary Medicine, 1999
- Primary pulmonary hypertensionThe Lancet, 1998
- Pulmonary Edema Complicating Continuous Intravenous Prostacyclin in Pulmonary Capillary HemangiomatosisAmerican Journal of Respiratory and Critical Care Medicine, 1998
- Pulmonary Capillary HemangiomatosisJournal of Thoracic Imaging, 1998
- Pulmonary Capillary Hemangiomatosis as a Rare Cause of Pulmonary HypertensionPathology - Research and Practice, 1996
- Treatment of Pulmonary Hemangiomatosis with Recombinant Interferon Alfa-2aThe New England Journal of Medicine, 1989
- Familial Pulmonary Capillary Hemangiomatosis Resulting in Primary Pulmonary HypertensionAnnals of Internal Medicine, 1988
- Capillary haemangiomatosis of the lungsHistopathology, 1978