Cystic Fibrosis F508del Patients Have Apically Localized CFTR in a Reduced Number of Airway Cells
- 1 June 2000
- journal article
- Published by Elsevier BV in Laboratory Investigation
- Vol. 80 (6), 857-868
- https://doi.org/10.1038/labinvest.3780090
Abstract
No abstract availableKeywords
This publication has 63 references indexed in Scilit:
- Modified epithelial cell distribution in chronic airways inflammationEuropean Respiratory Journal, 1996
- A delta F508 mutation in mouse cystic fibrosis transmembrane conductance regulator results in a temperature-sensitive processing defect in vivo.JCI Insight, 1996
- A 32-bp deletion (2991del32) in the cystic fibrosis gene associated with CFTR mRNA reductionHuman Mutation, 1994
- Plasma membrane recycling in CFTR-expressing CHO cellsBiochimica et Biophysica Acta (BBA) - Molecular Basis of Disease, 1993
- Localization of cystic fibrosis transmembrane conductance regulator in chloride secretory epithelia.JCI Insight, 1992
- Altered chloride ion channel kinetics associated with the ΔF508 cystic fibrosis mutationNature, 1991
- Measurement of nasal potential difference in adult cystic fibrosis, Young's syndrome, and bronchiectasis.Thorax, 1987
- Transepithelial potential difference in cystic fibrosis.Thorax, 1985
- Increased Bioelectric Potential Difference across Respiratory Epithelia in Cystic FibrosisNew England Journal of Medicine, 1981
- NON-INVASIVE SAMPLING OF NASAL CILIA FOR MEASUREMENT OF BEAT FREQUENCY AND STUDY OF ULTRASTRUCTUREThe Lancet, 1980