Polyarteritis nodosa in case of familial mediterranean fever
- 1 January 2018
- journal article
- research article
- Published by Hacettepe University Institute of Child Health in The Turkish Journal of Pediatrics
- Vol. 60 (3), 326-330
- https://doi.org/10.24953/turkjped.2018.03.016
Abstract
Familial Mediterranean fever (FMF) is an autosomal recessive disease characterized by recurrent self-limited attacks of fever accompanied by peritonitis, pleuritis, and arthritis. Protracted febrile myalgia syndrome (PFMS) is a rare form of vasculitic disease which is an uncommon dramatic manifestation of FMF, characterized by severe crippling myalgia and high fever. Polyarteritis nodosa (PAN) is a systemic necrotizing vasculitis affecting medium or small arteries. It is rarely observed in children, but its incidence increases in the presence of FMF. In this article we described a 14-yea-old child diagnosed with FMF associated with PAN. Physicians should be aware of this possible association.Keywords
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