Anaesthesia for liver transplantation in a patient with methylmalonic acidaemia
- 1 February 2000
- journal article
- case report
- Published by Wiley in Pediatric Anesthesia
- Vol. 10 (2), 215-218
- https://doi.org/10.1046/j.1460-9592.2000.00451.x
Abstract
Liver transplantation is an accepted modality of treatment in some patients with inborn errors of metabolism. We present a child with methylmalonic acidaemia who had successful liver transplantation. The pathophysiology, medical and anaesthetic managements are discussed.Keywords
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