Churg-Strauss Syndrome Complicated by Chronic Periaortitis: A Case Report and Review of the Literature
Open Access
- 1 January 2012
- journal article
- case report
- Published by Japanese Society of Internal Medicine in Internal Medicine
- Vol. 51 (1), 109-112
- https://doi.org/10.2169/internalmedicine.51.5985
Abstract
We present a case of Churg-Strauss syndrome complicated by chronic periaortitis. A 68-year-old man presented with wheezing, dyspnea, purpurae, and numbness of the extremities. Antineutrophil cytoplasmic antibodies were absent; however, eosinophilia, a pulmonary infiltrative shadow on chest X-ray, eosinophilic vasculitis on histologic examination of skin and kidney, and mononeuritis multiplex were detected. Churg-Strauss syndrome was diagnosed. Contrast-enhanced abdominal computed tomography revealed a periaortic soft tissue mass extending from the subphrenic abdominal aorta to the proximal area of the bilateral iliac arteries. This indicated chronic periaortitis, probably caused by vasculitic activities. Both disorders improved with steroid therapy.Keywords
This publication has 20 references indexed in Scilit:
- p-ANCA-associated periaortitis with histological proof of Wegener’s granulomatosis: case reportClinical Rheumatology, 2004
- Chronic periaortitisRheumatology, 2004
- Evidence of autoimmunity in chronic periaortitis: a prospective studyAmerican Journal Of Medicine, 2003
- Study of 52 patients with idiopathic aortitis from a cohort of 1,204 surgical casesArthritis & Rheumatism, 2000
- Periaortitis and Aortic Dissection due to Wegener's GranulomatosisClinical Rheumatology, 2000
- Indium-111 labelled leucocyte uptake in aortitisClinical Radiology, 1994
- Nomenclature of Systemic VasculitidesArthritis & Rheumatism, 1994
- Retroperitoneal fibrosis after surgery for aortic aneurysm in a patient with periarteritis nodosa: successful treatment with corticosteroidsJournal of Internal Medicine, 1990
- The spectrum of chronic periaortitisHistopathology, 1990
- Henoch-Schönlein Purpura and Retroperitoneal FibrosisActa Haematologica, 1983