Bioenergetics in Glutaryl-Coenzyme A Dehydrogenase Deficiency
Open Access
- 1 June 2005
- journal article
- Published by Elsevier BV
- Vol. 280 (23), 21830-21836
- https://doi.org/10.1074/jbc.m502845200
Abstract
No abstract availableThis publication has 62 references indexed in Scilit:
- Inhibition of the α‐ketoglutarate dehydrogenase complex by the myeloperoxidase products, hypochlorous acid and mono‐N‐chloramineJournal of Neurochemistry, 2005
- Evidence that 3-hydroxyglutaric acid interacts with NMDA receptors in synaptic plasma membranes from cerebral cortex of young ratsNeurochemistry International, 2004
- Methylmalonic Acid, a Biochemical Hallmark of Methylmalonic Acidurias but No Inhibitor of Mitochondrial Respiratory ChainPublished by Elsevier BV ,2003
- Chronic treatment with glutaric acid induces partial tolerance to excitotoxicity in neuronal cultures from chick embryo telencephalonsJournal of Neuroscience Research, 2002
- Brain regional development of the activity of α-ketoglutarate dehydrogenase complex in the ratDevelopmental Brain Research, 2000
- Association between the gene encoding the E2 subunit of the α‐ketoglutarate dehydrogenase complex and Parkinson's diseaseAnnals of Neurology, 1998
- Inhibitory effect of 3‐hydroxyacyl‐CoAs and other long‐chain fatty acidβ‐oxidation intermediates on mitochondrial oxidative phosphorylationJournal of Inherited Metabolic Disease, 1996
- Abnormality of the α‐ketoglutarate dehydrogenase complex in fibroblasts from familial Alzheimer's diseaseAnnals of Neurology, 1994
- An immunohistochemical study on α‐ketoglutarate dehydrogenase complex in Parkinson's diseaseAnnals of Neurology, 1994
- Glutaric aciduria: Biochemical and morphologic considerationsThe Journal of Pediatrics, 1977