An Official ATS/ERS/JRS/ALAT Statement: Idiopathic Pulmonary Fibrosis: Evidence-based Guidelines for Diagnosis and Management
Top Cited Papers
- 15 March 2011
- journal article
- practice guideline
- Published by American Thoracic Society in American Journal of Respiratory and Critical Care Medicine
- Vol. 183 (6), 788-824
- https://doi.org/10.1164/rccm.2009-040gl
Abstract
This document is an international evidence-based guideline on the diagnosis and management of idiopathic pulmonary fibrosis, and is a collaborative effort of the American Thoracic Society, the European Respiratory Society, the Japanese Respiratory Society, and the Latin American Thoracic Association. It represents the current state of knowledge regarding idiopathic pulmonary fibrosis (IPF), and contains sections on definition and epidemiology, risk factors, diagnosis, natural history, staging and prognosis, treatment, and monitoring disease course. For the diagnosis and treatment sections, pragmatic GRADE evidence-based methodology was applied in a question-based format. For each diagnosis and treatment question, the committee graded the quality of the evidence available (high, moderate, low, or very low), and made a recommendation (yes or no, strong or weak). Recommendations were based on majority vote. It is emphasized that clinicians must spend adequate time with patients to discuss patients' values and preferences and decide on the appropriate course of action.Keywords
This publication has 309 references indexed in Scilit:
- A Controlled Trial of Sildenafil in Advanced Idiopathic Pulmonary FibrosisThe New England Journal of Medicine, 2010
- Epidemiology of interstitial lung diseases in GreeceRespiratory Medicine, 2009
- Genetic Defects in Surfactant Protein A2 Are Associated with Pulmonary Fibrosis and Lung CancerAmerican Journal of Human Genetics, 2009
- Right ventricular systolic pressure by echocardiography as a predictor of pulmonary hypertension in idiopathic pulmonary fibrosisRespiratory Medicine, 2008
- Short telomeres are a risk factor for idiopathic pulmonary fibrosisProceedings of the National Academy of Sciences of the United States of America, 2008
- Adult-onset pulmonary fibrosis caused by mutations in telomeraseProceedings of the National Academy of Sciences of the United States of America, 2007
- Racial and Ethnic Disparities in Idiopathic Pulmonary Fibrosis: A UNOS/OPTN Database AnalysisAmerican Journal of Transplantation, 2006
- ELMOD2 Is a Candidate Gene for Familial Idiopathic Pulmonary FibrosisAmerican Journal of Human Genetics, 2006
- Familial Idiopathic Pulmonary FibrosisThe New England Journal of Medicine, 1986
- Prognosis of cryptogenic fibrosing alveolitis.Thorax, 1983