Parenchymal organ cystine depletion with long-term cysteamine therapy
- 31 December 1992
- journal article
- case report
- Published by Elsevier BV in Biochemical Medicine and Metabolic Biology
- Vol. 48 (3), 275-285
- https://doi.org/10.1016/0885-4505(92)90074-9
Abstract
No abstract availableKeywords
This publication has 23 references indexed in Scilit:
- Swallowing Dysfunction in Nephropathic CystinosisThe New England Journal of Medicine, 1990
- Neurologic Complications in Long-standing Nephropathic CystinosisArchives of Neurology, 1989
- Myopathy and Cystine Storage in Muscles in a Patient with Nephropathic CystinosisThe New England Journal of Medicine, 1988
- A Comparison of the Effectiveness of Cysteamine and Phosphocysteamine in Elevating Plasma Cysteamine Concentration and Decreasing Leukocyte Free Cystine in Nephropathic CystinosisPediatric Research, 1988
- Pancreatic exocrine insufficiency in a patient with nephropathic cystinosisThe Journal of Pediatrics, 1988
- Cystine storage in cultured myotubes from patients with nephropathic cystinosisBiochemical Journal, 1987
- Course of nephropathic cystinosis after age 10 yearsThe Journal of Pediatrics, 1986
- Cystine Transport Is Defective in Isolated Leukocyte Lysosomes from Patients with CystinosisScience, 1982
- Cystine depletion of cystinotic tissues by phosphocysteamine (WR638)The Journal of Pediatrics, 1980
- Cystinosis. Intracellular cystine depletion by aminothiols in vitro and in vivo.JCI Insight, 1976