Successful initiation and maintenance of hemodialysis in an adult patient with complete transposition of the great arteries
- 6 July 2010
- journal article
- case report
- Published by Springer Science and Business Media LLC in Clinical and Experimental Nephrology
- Vol. 14 (5), 511-515
- https://doi.org/10.1007/s10157-010-0315-y
Abstract
Cyanotic congenital heart disease (CCHD) is a life-threatening cardiac defect that requires palliative or corrective surgery in early life. Major advances in medical and surgical management have resulted in the survival of CCHD patients to adulthood with or without corrective surgery, though some are at risk of development of end-stage renal disease (ESRD) due to cyanotic nephropathy (CN). There is little or no information on the initiation and maintenance of hemodialysis (HD) in such patients. We present here a case of a 44-year-old man with complete transposition of the great arteries and CN-related ESRD. He had only received a bi-directional Glenn's operation and still suffered persistent severe hypoxemia and impaired cardiac function. ESRD was successfully treated with HD over more than 4 years. The case emphasizes the need for special attention in the selection and initiation of renal replacement therapy.Keywords
This publication has 14 references indexed in Scilit:
- Predictive factors for long-term prognosis in adults with cyanotic congenital heart disease — Japanese multi-center studyInternational Journal of Cardiology, 2007
- Cardiovascular disease in haemodialysis and peritoneal dialysis: arguments pro haemodialysisNephrology Dialysis Transplantation, 2006
- Mechanisms of development and progression of cyanotic nephropathyPediatric Nephrology, 2006
- 2005 Japanese Society for Dialysis Therapy Guidelines for Vascular Access Construction and Repair for Chronic HemodialysisTherapeutic Apheresis and Dialysis, 2006
- Current patterns of infective endocarditis in congenital heart diseaseHeart, 2006
- Survey of specialized tertiary care facilities for adults with congenital heart diseaseInternational Journal of Cardiology, 2004
- Partial exchange transfusion improved renal function and proteinuria in a patient with cyanotic heart disease nephropathyClinical Nephrology, 2003
- Nephropathy of cyanotic congenital heart disease: clinical characteristics and effectiveness of an angiotensin-converting enzyme inhibitorClinical Nephrology, 2002
- Cyanotic congenital heart disease associated with glomerulomegaly and focal segmental glomerulosclerosis: remission of nephrotic syndrome with angiotensin converting enzyme inhibitorNephrology Dialysis Transplantation, 2002
- Pulmonary/systemic flow ratio in children after cavopulmonary anastomosisJournal of the American College of Cardiology, 1995