Intimal pulmonary artery sarcoma presenting as dyspnea: case report
Open Access
- 29 June 2007
- journal article
- Published by Springer Science and Business Media LLC in International Seminars in Surgical Oncology
- Vol. 4 (1), 14
- https://doi.org/10.1186/1477-7800-4-14
Abstract
We report a case of pulmonary sarcoma which is a rare cause of the common symptom of dyspnea. A fifty-one year old previously healthy male presented to the emergency room with complaints of dyspnea on exertion. A cardiac workup including an exercise stress test was negative but an echocardiography showed pulmonary stenosis. Cardiac MRI showed a large mass extending from the pulmonic valve to both the right and left pulmonary arteries suggestive of sarcoma. A complete resection and repair of the pulmonary artery was done and adjuvant chemotherapy with doxorubicin and ifosfamide was recommended. The patient is currently disease free after eighteen months. Pulmonary artery sarcomas are a difficult diagnosis. The diagnosis may remain elusive for some time until the proper imaging techniques are utilized to make a diagnosis. Earlier and accurate diagnosis may lead to earlier interventions and improve survival.Keywords
This publication has 10 references indexed in Scilit:
- A Case of Pulmonary Artery Intimal Sarcoma Diagnosed with Multislice CT Scan with 3D ReconstructionYonsei Medical Journal, 2004
- Intimal Sarcoma of the Pulmonary Arteries Seen as a Mosaic Pattern of Lung Attenuation on High-Resolution CTAmerican Journal of Roentgenology, 2002
- Right pulmonary artery sarcomaPathology, 2001
- Adjuvant chemotherapy for localised resectable soft-tissue sarcoma of adults: meta-analysis of individual data. Sarcoma Meta-analysis Collaboration.1997
- Adjuvant chemotherapy for localised resectable soft-tissue sarcoma of adults: meta-analysis of individual dataThe Lancet, 1997
- Chemotherapy for advanced sarcoma: therapeutic decisions and modalities.1997
- Sarcomas related to the heart and vasculatureSeminars in Surgical Oncology, 1994
- Sarcoma of the pulmonary artery: report of four cases with electron microscopic and immunohistochemical examinations, and review of the literatureVirchows Archiv A Pathological Anatomy and Histopathology, 1994
- Sarcomas of the great vessels. A clinicopathologic studyCancer, 1993
- Pulmonary Artery SarcomaJournal of Computer Assisted Tomography, 1990