Hypertrophic pachymeningitis as an important neurological complication of granulomatosis with polyangiitis
Open Access
- 23 December 2018
- journal article
- review article
- Published by Termedia Sp. z.o.o. in Rheumatology
- Vol. 56 (6), 399-405
- https://doi.org/10.5114/reum.2018.80719
Abstract
Headache is a common symptom in patients with granulomatosis with polyangiitis (GPA) mainly due to chronic sinusitis or orbital disease. Meningeal involvement may thus remain unrecognized for a long time. This can lead to a significant delay in accurate diagnosis, serious local damage of the central nervous system and high relapse rates. New diagnostic techniques such as contrast MRI allow one to identify inflammation of the dura mater in the course of GPA more frequently. The objective of this article is to characterize hypertrophic pachymeningitis (HP) in patients with GPA and report diagnostic difficulties associated with this complication.Keywords
This publication has 31 references indexed in Scilit:
- Pachymeningitis in Granulomatosis with Polyangiitis: A Case Report and a Review of the LiteratureCase Reports in Rheumatology, 2013
- Hypertrophic pachymeningitis and cerebral infarction resulting from ANCA-associated vasculitisNeurology India, 2012
- Neurological involvement in Wegener's granulomatosisCurrent Opinion in Rheumatology, 2011
- Cranial pachymeningitis: a rare neurological syndrome with heterogeneous aetiologyJournal of Neurology, Neurosurgery & Psychiatry, 2010
- Diffuse intracranial meningeal enhancement in Wegener's granulomatosis—A rare findingEuropean Journal of Radiology Extra, 2008
- Central Nervous System Involvement in Wegener GranulomatosisMedicine, 2006
- Aneurysmal subarachnoid hemorrhage in a patient with Wegener?s granulomatosisClinical and Experimental Nephrology, 2004
- Limited versus severe Wegener's granulomatosis: Baseline data on patients in the Wegener's granulomatosis etanercept trialArthritis & Rheumatism, 2003
- Neurological involvement in Wegener's granulomatosis: An analysis of 324 consecutive patients at the Mayo ClinicAnnals of Neurology, 1993
- Neurological Complications of Wegener's GranulomatosisArchives of Neurology, 1963