Oesophageal atresia and associated anomalies.
Open Access
- 1 March 1989
- journal article
- research article
- Published by BMJ in Archives of Disease in Childhood
- Vol. 64 (3), 364-368
- https://doi.org/10.1136/adc.64.3.364
Abstract
Of 253 infants with oesophageal atresia treated over an eight year period, 122 (48%) had a total of 213 other anomalies. Most commonly affected were the cardiovascular (61 cases, 29%), anorectal (30 cases, 14%), and genitourinary (29 cases, 14%) systems. The VATER (or VACTERL) association was present in 10% of cases, but occurred more often in patients who had oesophageal atresia without an associated tracheo-oesophageal fistula (3/13, 23%). The level of the associated anorectal malformation was not associated with the type of oesophageal atresia. The presence and severity of other anomalies did not influence the basic approach to treatment of the oesophageal atresia--that is, primary repair whenever possible. Despite aggressive treatment, cardiac malformations were the most common cause of death. There were five infants with the CHARGE association, two with Potter's syndrome, and two with 'SCHISIS' syndrome (cleft lip and palate, omphalocoele, and hypogenitalism).Keywords
This publication has 20 references indexed in Scilit:
- Esophageal atresia: Five year experience with 148 casesJournal of Pediatric Surgery, 1987
- Coloboma, congenital heart disease, and choanal atresia with multiple anomalies: CHARGE associationThe Journal of Pediatrics, 1981
- Combined esophageal and duodenal atresia: Experience of 18 patientsJournal of Pediatric Surgery, 1981
- Schisis-associationAmerican Journal of Medical Genetics, 1981
- Surgical experience in infants with the VATER associationJournal of Pediatric Surgery, 1980
- Esophageal atresia and associated anomaliesJournal of Pediatric Surgery, 1976
- Extending the scope of the VATER association: Definition of the VATER syndromeThe Journal of Pediatrics, 1974
- The VATER association: -Vertebral defects, -Anal atresia, -T-Efistula with esophageal atresia, -Radial and -Renal dysplasia: A spectrum of associated defectsThe Journal of Pediatrics, 1973
- CONGENITAL TRACHEO-ŒSOPHAGEAL FISTULA IN ASSOCIATION WITH ŒSOPHAGEAL ATRESIAThe Lancet, 1963
- $OElig;SOPHAGEAL ATRESIA: TRACHEO-$OElig;SOPHAGEAL FISTULA A Study of Survival in 218 InfantsThe Lancet, 1962