Metastasizing Eccrine Porocarcinoma Developing in a Sebaceous Nevus of Jadassohn

Abstract

Sebaceous nevus of Jadassohn(SNJ) is an organoid hamartoma of the skin that is usually seen at or shortly after birth. Its most common location is the scalp, however, it may involve other areas of the head and neck. The SNJ characteristically evolves and changes morphology with time.¹The development of neoplasms in SNJ is well documented to the degree of regarding such a development as part of the natural history of the lesion.²Usually these are benign neoplasms of epidermal or skin adnexal origin, but the development of malignant tumors have also been reported. We are reporting an additional case of a metastasizing neoplasm developing in SNJ to emphasize the aggressive neoplastic potential of these hamartomas. Report of a Case A 45-year-old man was seen at Kings County (New York) Hospital in September 1982 with a nodular scalp lesion. The patient described the existence of an alopecic,