Familial Gigantiform Cementoma
- 1 March 1999
- journal article
- research article
- Published by Ovid Technologies (Wolters Kluwer Health) in Plastic and Reconstructive Surgery
- Vol. 103 (3), 949-954
- https://doi.org/10.1097/00006534-199903000-00027
Abstract
Familial gigantiform cementoma is a rare autosomal dominant tumor that is benign but can result in disfigurement of the facial skeleton. Two families with a total of five patients presented for treatment. Because of a lack of opportunity to obtain treatment early, three of the patients presented in adult life with massive tumors requiring extensive resection and complex reconstruction in multiple stages. The two female patients had chronic anemia caused by multifocal polypoid adenomas of the uterus and required hysterectomy before treatment. The last three patients had elevated alkaline phosphatase levels before tumor resection, and these levels decreased after surgery. With extensive resection of the tumors and reconstruction of both the soft tissues and facial skeleton, good functional and aesthetic results can be obtained. There has been no tumor recurrence with 3 years of follow-up. (Plast. Reconstr. Surg. 103: 949, 1999.)Keywords
This publication has 9 references indexed in Scilit:
- Gigantiform cementoma affecting a Caucasian familyBritish Journal of Oral and Maxillofacial Surgery, 1991
- Gigantiform cementoma showing apparent activity on a bone scan.Dentomaxillofacial Radiology, 1990
- Familial gigantiform cementoma: Classification and presentation of a large pedigreeOral Surgery, Oral Medicine, Oral Pathology, 1989
- Gigantiform cementoma of the jawsHead & Neck, 1989
- Florid cemento-osseous dysplasia (gigantiform cementoma) in a caucasian womanBritish Journal of Oral and Maxillofacial Surgery, 1989
- Gigantiform Cementoma. Report of 2 CasesDentomaxillofacial Radiology, 1987
- Gigantiform cementoma—an unusual incidental findingThe British Journal of Radiology, 1986
- Gigantiform cementoma: Review of the literature and a case reportBritish Journal of Oral Surgery, 1980
- A case of gigantiform cementomaInternational Journal of Oral Surgery, 1974