Extramammary Pagetʼs Disease of the Oral Mucosa with In Situ Carcinoma of Minor Salivary Gland Ducts

Abstract

This paper describes a case of oral extramammary Paget's disease associated with widespread in situ carcinoma of minor salivary gland ducts and invasive, poorly differentiated carcinoma. Clinically, the case was characterized by unusually extensive and rapidly spreading erythroplakia of the oral mucosa, accompanied by a relatively small invasive salivary gland carcinoma. Despite the similarities of breast and salivary tissue, oral extramammary Paget's disease appears to be extremely rare.