Heparan sulfate and dermatan sulfate from the liver of a patient with Hurler syndrome: high performance liquid chromatography of their degradation products after incubation with α-l-iduronidase-deficient fibroblasts
- 1 February 1984
- journal article
- research article
- Published by Elsevier BV in Clinica Chimica Acta; International Journal of Clinical Chemistry
- Vol. 137 (2), 179-187
- https://doi.org/10.1016/0009-8981(84)90178-5
Abstract
No abstract availableKeywords
This publication has 13 references indexed in Scilit:
- Structural differences of heparan sulfates according to the tissue and species of originBiochemical and Biophysical Research Communications, 1983
- Characterization of keratan sulfate isolated from liver affected by Morquio syndrome.The Tohoku Journal of Experimental Medicine, 1983
- Acidic glycosaminoglycans and gangliosides in the brains from four patients with genetic mucopolysaccharidosis.The Tohoku Journal of Experimental Medicine, 1982
- Separation of reduced disaccharides derived from glycosaminoglycans by high-performance liquid chromatographyJournal of Chromatography A, 1981
- Prenatal diagnosis of Hurler's syndrome?Biochemical studies on the affected fetusHuman Genetics, 1981
- Enzymatic studies of urinary isomeric chondroitin sulfates from patients with mucopolysaccharidoses. The application of high performance liquid chromatographyClinica Chimica Acta; International Journal of Clinical Chemistry, 1980
- Fluorometric measurement of .ALPHA.-L-iduronidase activity using 4-methylumbelliferyl-.ALPHA.-L-iduronide.The Tohoku Journal of Experimental Medicine, 1980
- A fluorometric assay using 4-methylumbelliferyl α-l-iduronide for the estimation of α-l-iduronidase activity and the detection of Hurler and Scheie syndromesClinica Chimica Acta; International Journal of Clinical Chemistry, 1979
- GLUCOSE-6-PHOSPHATASE IN HUMAN PLACENTA: A NEW METHOD FOR THE STUDY OF GLYCOGEN STORAGE DISEASE TYPE I. POSSIBLE IDENTIFICATION OF A HETEROZYGOTEPediatric Research, 1977
- A rapid and micro method for separation of acidic glycosaminoglycans by two-dimensional electrophoresisAnalytical Biochemistry, 1972