Primary subcutaneous sacrococcygeal ependymoma: a case report and review of the literature
- 1 May 2006
- journal article
- case report
- Published by Oxford University Press (OUP) in The British Journal of Radiology
- Vol. 79 (941), 445-447
- https://doi.org/10.1259/bjr/61959899
Abstract
Extraspinal ependymomas are rare. The majority occur in the sacrococcygeal region. The subcutaneous variety accounts for approximately two thirds of cases, which are commonly misdiagnosed as a pilonidal cyst or sinus. Treatment is complete surgical resection. The role of coccygectomy is controversial. Adjuvant radiotherapy is of benefit to those with an incompletely excised tumour. Up to 20% metastasise, chiefly to the inguinal lymph glands, but pulmonary metastases are also reported. Palliative chemotherapy has not been shown to be of any benefit. Long term follow-up is important as metastases can occur up to 20 years after initial presentation. We report a 37-year-old woman with a subcutaneous sacrococcygeal ependymoma with iliac lymph nodal metastasis at presentation.Keywords
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