Isolated Unilateral Pulmonary Vein Atresia in Adult Patients: A Case Report and Literature Review
- 1 December 2010
- journal article
- case report
- Published by Carden Jennings Publishing Co. in The Heart Surgery Forum
- Vol. 13 (6), E370-E372
- https://doi.org/10.1532/hsf98.20101078
Abstract
Unilateral pulmonary vein atresia is a rare abnormality that usually presents in infants with recurrent hemoptysis and pneumonia. Presentation in adulthood without additional congenital heart disease is rare but does occur. Anatomic variations in the pulmonary vessels that supply and drain the affected lung can explain the mildly symptomatic process. The diagnosis of isolated unilateral pulmonary vein atresia is usually made angiographically. Pneumonectomy is indicated once symptoms or complications are present so that irreversible pulmonary hypertension can be avoided.Keywords
This publication has 10 references indexed in Scilit:
- CT angiography of mildly symptomatic, isolated, unilateral right pulmonary vein atresiaPediatric Radiology, 2009
- Bronchoscopic Diagnosis of Asymptomatic Unilateral Pulmonary Vein Atresia in an InfantPediatric Cardiology, 2007
- Atresia of Right Pulmonary Veins with Intact Atrial Septum and Major Aorto-Pulmonary Collateral Treated with Percutaneous Stent Implantation and EmbolizationJournal of Interventional Cardiology, 2004
- Congenital Unilateral Pulmonary Venous Atresia: Definitive Diagnosis and TreatmentPediatric Cardiology, 2003
- Congenital Unilateral Pulmonary Vein AtresiaAmerican Journal of Roentgenology, 2001
- Esophageal varices in association with unilateral pulmonary vein atresiaCatheterization and Cardiovascular Diagnosis, 1996
- Improved gas exchange after pneumonectomy in an adult with incomplete pulmonary vein atresia.Thorax, 1994
- Isolated pulmonary vein atresia.Heart, 1990
- Isolated atresia of the left pulmonary veinsInternational Journal of Cardiology, 1985
- Unilateral absence or extreme hypoplasia of pulmonary veins.Heart, 1983