Double Pathology in Rasmussen's Encephalitis: Etiologic Considerations
- 1 May 1996
- Vol. 37 (5), 495-500
- https://doi.org/10.1111/j.1528-1157.1996.tb00597.x
Abstract
In a 7-year-old girl with epilepsia partialis continua (EPC) involving the left face, arm, and leg for 1 year, serial neuroimaging studies showed progressive, brain atrophy. Because medical treatment was ineffective, she underwent a large fronto-temporal surgical resection. Neuropathological examination showed loss of lamination and dysplastic neurons, gliosis, microglial nodules, and perivascular cuffing. Such "double pathology" (dysgenesia and a chronic inflammatory process) may have implications for the pathophysiology of Rasmussen's syndrome.This publication has 6 references indexed in Scilit:
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