Spinal arteriovenous malformation associated with spinal metameric syndrome: a treatable cause of long-term paraplegia?
- 1 April 2012
- journal article
- Published by Journal of Neurosurgery Publishing Group (JNSPG) in Journal of Neurosurgery: Spine
- Vol. 16 (4), 408-413
- https://doi.org/10.3171/2011.12.spine11636
Abstract
Cutaneomeningospinal angiomatosis, or Cobb syndrome, is a rare metameric developmental disorder presenting as an extradural-intradural vascular malformation that involves bone, muscle, skin, spinal cord, and nerve roots. A 14-year-old girl with a red nevus involving the T6-9 dermatomes on the left side of her back presented with a 5-year history of bowel and bladder incontinence, paraplegia, and lower-extremity sensory loss. Magnetic resonance imaging demonstrated a hemangioma in the T-8 and T-9 vertebral bodies and a spinal cord AVM nidus extending from T-6 to T-9. The AVM was successfully embolized and the patient regained lower-extremity strength, ambulation, and normal sphincter functions after 5 years of having been wheelchair bound. The authors report the restoration of ambulation after endovascular embolization of a large spinal AVM in a patient with long-standing paraplegia due to Cobb syndrome.Keywords
This publication has 29 references indexed in Scilit:
- Cobb Syndrome: Case Report and Review of the LiteratureDermatology, 2010
- Recovery from paraplegia after the treatment of spinal dural arteriovenous fistula: case report and review of the literatureActa Neurochirurgica, 2009
- Curable Cause of ParaplegiaStroke, 2008
- Acute paralysis in a 17-year-old man with subtle cutaneous vascular malformations: an unusual case of Cobb syndromeJournal of the European Academy of Dermatology and Venereology, 2008
- Cobb Syndrome in an Indian GirlSKINmed: Dermatology for the Clinician, 2006
- Segmental cutaneous hemangioma and spinal arteriovenous malformation (Cobb syndrome)Journal of Neurosurgery: Spine, 2005
- Cobb Syndrome: Case ReportJournal of Child Neurology, 2002
- Cobb's syndrome and its treatment with embolizationJournal of Neurosurgery, 1990
- Cobb-Syndrom: Assoziation mit verrukösem Angiom, ipsilateraler Hypertrophie der Extremitäten und Café-au-lait-FleckenDermatology, 1981
- Cobb syndromeArchives of Dermatology, 1977