Most meningiomas are slow-growing tumors that do not rapidly recur after subtotal removal. After subtotal resection of a meningioma a 47-year-old woman developed a large extracranial recurrence 1 year later. The recurrence was resected successfully. On histological examination the typical characteristics of a meningioma were absent. Based on immunohistological and ultrastructural studies, the tumor was classified as a grade III meningioma of the newly recognized rhabdoid subtype. These tumors behave aggressively and should be treated accordingly.