Jugular foramen meningocoele in a patient with neurofibromatosis type 1
- 16 April 2007
- journal article
- case report
- Published by Cambridge University Press (CUP) in The Journal of Laryngology & Otology
- Vol. 122 (2), 213-216
- https://doi.org/10.1017/s0022215107007244
Abstract
Objective: We present a rare case of a jugular foramen meningocoele in a 48-year-old female, with neurofibromatosis type 1, presenting with positional vertigo. We also postulate possible underlying pathophysiological mechanisms.Method: We describe the imaging findings of this rare entity and review the literature on skull base meningocoeles, particularly in the context of neurofibromatosis type 1.Results: A computed tomography scan revealed smooth expansion of the jugular foramen. Magnetic resonance imaging showed a fluid filled lesion expanding the jugular foramen and communicating with cerebrospinal fluid of the cerebellomedullary cistern superiorly.Conclusion: Skull base meningocoeles are a rare entity and we believe that this is the first reported case of a meningocoele causing enlargement of the jugular foramen in a patient with neurofibromatosis type 1. The meningocoele may have resulted from a severe form of dural ectasia or from dysplastic, weakened bone at the skull base.Keywords
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