Pulmonary arteriovenous malformations: a clinical review
- 1 July 2000
- journal article
- case report
- Published by Oxford University Press (OUP)
- Vol. 76 (897), 390-394
- https://doi.org/10.1136/pmj.76.897.390
Abstract
Pulmonary arteriovenous malformations (PAVMs) are a rare clinical entity. Most of them are associated with hereditary haemorrhagic telangiectasia. The usual clinical presentation is exertional dyspnoea and hypoxaemia. The initial test of choice for screening is the 100% oxygen method. A pulmonary angiogram is needed to define the anatomy and guide transcatheter embolisation (TCE). TCE has been shown to be effective and safe with a very low recanalisation rate and has largely replaced surgery for PAVMs. Computed tomography of the chest can be used for the follow up of asymptomatic PAVMs and TCE.Keywords
This publication has 22 references indexed in Scilit:
- Pulmonary Arteriovenous Malformations: Diagnosis and Transcatheter EmbolotherapyJournal of Vascular and Interventional Radiology, 1996
- Mutations in the activin receptor–like kinase 1 gene in hereditary haemorrhagic telangiectasia type 2Nature Genetics, 1996
- Hereditary Hemorrhagic TelangiectasiaNew England Journal of Medicine, 1995
- Endoglin, a TGF-β binding protein of endothelial cells, is the gene for hereditary haemorrhagic telangiectasia type 1Nature Genetics, 1994
- A gene for hereditary haemorrhagic telangiectasia maps to chromosome 9q3Nature Genetics, 1994
- Quantification of right to left shunt at rest and during exercise in patients with pulmonary arteriovenous malformations.Thorax, 1992
- Two-dimensional contrast echocardiography in the detection and follow-up of congenital pulmonary arteriovenous malformationsThe American Journal of Cardiology, 1991
- Pulmonary Arteriovenous MalformationsNew England Journal of Medicine, 1983
- Continuous Distributions of Ventilation-Perfusion Ratios in Normal Subjects Breathing Air and 100% O2JCI Insight, 1974
- A nomogram for venous shunt (QS/QT) calculationThorax, 1968