Acute airway compromise and coagulopathy: a rare presentation of acquired haemophilia A
- 1 May 2020
- journal article
- research article
- Published by BMJ in BMJ Case Reports
- Vol. 13 (5), e233345
- https://doi.org/10.1136/bcr-2019-233345
Abstract
Acquired haemophilia A is a rare but important diagnosis, carrying a mortality rate of 22%. Life-threatening sequalae of this diagnosis includes airway compromise, which can rapidly lead to demise of the patient if left untreated. Our case examines an 80-year-old man presenting with a supraglottic haematoma resulting from acquired haemophilia A causing airway compromise and necessitating definitive airway control. A review of current understanding and management of the disease is also ddiscussed.This publication has 19 references indexed in Scilit:
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