Aortic Angiosarcoma: A Rare Cause for Leaking Thoracic Aneurysm
- 10 February 2010
- journal article
- case report
- Published by Springer Science and Business Media LLC in CardioVascular and Interventional Radiology
- Vol. 34 (2), 20-24
- https://doi.org/10.1007/s00270-009-9776-3
Abstract
Primary malignant tumours of the aorta are rare. They present with aneurysm formation, arterial occlusion, and embolic phenomenon. We report the case of a 56-year-old man whose initial presentation and investigations lead to emergency endovascular stenting of a descending thoracic aneurysm with a contained leak. Initial response was favourable, yet the patient presented again with worsening symptoms. The circum-aortic haematoma expanded by 50% on subsequent imaging, but no endoleak was identified. When altered bone marrow signal was identified on magnetic resonance imaging, the possibility of malignancy was considered. A metastatic skin lesion was then biopsied, which demonstrated morphological and immunohistochemical features consistent with metastases from a pleomorphic sarcoma of the aorta.Keywords
This publication has 13 references indexed in Scilit:
- Endovascular Stent Graft Placement in the Treatment of Ruptured Tuberculous Pseudoaneurysm of the Descending Thoracic Aorta: Case Report and Review of the LiteratureCardioVascular and Interventional Radiology, 2008
- Long-Term Follow-Up After Endovascular Treatment of Acute Aortic EmergenciesCardioVascular and Interventional Radiology, 2007
- In Vitro Evaluation of Current Thoracic Aortic Stent-Grafts for Real-time MR-Guided PlacementJournal of Endovascular Therapy, 2006
- Primary sarcoma of an abdominal aortic aneurysmAbdominal Radiology, 2005
- Undifferentiated Intimal Sarcoma of Large Systemic Blood VesselsThe American Journal of Surgical Pathology, 2005
- Intimal angiosarcoma of the aorta: Report of a case and review of the literatureJournal of Vascular Surgery, 2004
- Primary Tumors of the Thoracoabdominal Aorta: Surgical Treatment of 5 Patients and Review of the LiteratureAnnals of Vascular Surgery, 2003
- Intimal Sarcoma of the AortaAmerican Journal of Roentgenology, 2000
- Intimal-type primary sarcoma of the thoracic aorta presenting as a saccular false aneurysm: Report of a case with evidence of rhabdomyosarcomatous differentiationThe Journal of Thoracic and Cardiovascular Surgery, 1999
- Aortic intimal sarcoma with embolic metastasesThe American Journal of Surgical Pathology, 1985