Focal segmental glomerulosclerosis in patients after Fontan operation: is this a Fontan-associated renal disease?
- 15 September 2021
- journal article
- research article
- Published by Cambridge University Press (CUP) in Cardiology in the Young
- Vol. 32 (5), 837-839
- https://doi.org/10.1017/s1047951121003929
Abstract
Despite acceptable survival for Fontan operation, there are concerns about late complications affecting the major organs. We herein present two cases of adults after Fontan operation who developed focal segmental glomerulosclerosis. These cases suggest that focal segmental glomerulosclerosis is owing to haemodynamic incompetence associated with Fontan operation, including congestion, hypoxia, and hyperviscosity, which may be called Fontan-associated renal disease.Keywords
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