Extra-axial, dural-based atypical teratoid/rhabdoid tumor
- 4 May 2021
- journal article
- research article
- Published by Springer Science and Business Media LLC in Child's Nervous System
- Vol. 38 (3), 655-658
- https://doi.org/10.1007/s00381-021-05196-7
Abstract
Atypical teratoid/rhabdoid tumors (ATRTs) are malignant central nervous system tumors that affect early childhood (< 3 years), and mostly located in the infratentorial space. Owing to an infrequent occurrence, their radiological features have not been completely defined. Nevertheless, these are characteristically intra-axial except for few instances in the cerebellopontine angle region. We describe a case of a 10-year-old boy who harbored an extra-axial, dural-based ATRT in the right parietal region. The lesion was totally excised followed by adjuvant chemo-radiotherapy. At 10-month follow-up, he was well with no recurrence. The report intends to highlight an atypical imaging presentation of ATRT in an older child, and adds to the radiological spectrum. This uncommon pathology should be borne in mind, even in a supratentorial dural-based location.This publication has 17 references indexed in Scilit:
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