OUR EXPERIENCE IN TREATMENT OF HIRSCHSPRUNG'S DISEASE IN A 18-YEAR-OLD PATIENT. CLINICAL CASE
Open Access
- 19 April 2021
- journal article
- Published by Center of Endourology Endocenter in Surgical practice (Russia)
- No. 1,p. 47-52
- https://doi.org/10.38181/2223-2427-2020-4-47-52
Abstract
Introduction: Hirschsprung's disease (HD) is a relatively rare condition, in which the intermuscular (Auerbach) and submucosal (Meissner) plexus are absent in the colon wall at various lengths. In the literature, HD is described mainly in relation to the pediatric surgery area of interests because up to 90% of cases of this disease are detected before the age of 5 years 6. However, in some patients, the symptoms of the disease are not severe, so patients survive to adulthood without an established diagnosis.Clinical case: we demonstrate our experience of surgical treatment of Hirschsprung's disease in a 18-year-old patient.Conclusion: Although Hirschsprung's disease is in most cases a disease of childhood, it is necessary to keep in mind its typical symptoms when an adult patient complains of constipation. Proper diagnosis and correctly selected surgical treatment can not only eliminate symptoms and improve quality of life, but also reduce the likelihood of serious complications.Keywords
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