Retroperitoneal Spindle Cell Rhabdomyosarcoma With Compression Features in a 48-Year-Old Male: A Case Report
Open Access
- 26 September 2022
- journal article
- research article
- Published by Springer Science and Business Media LLC in Cureus
- Vol. 14 (9)
- https://doi.org/10.7759/cureus.29622
Abstract
Spindle cell rhabdomyosarcoma (SC-RMS) is an unprecedented version of embryonal rhabdomyosarcomas (RMSs) that emerges from the mesenchyme with the capacity to differentiate into skeletal muscle cells. Retroperitoneal RMS is extremely rare in the adult population. We present the case of a primary spindle cell retroperitoneal RMS with compression features. Investigation-based diagnosis of RMS is difficult due to the lack of specificity of clinical findings. Radiology does not help in making an accurate diagnosis. Surgical removal of the tumor followed by chemotherapy and radiotherapy is the best possible treatment for RMS in adults. SC-RMS has a poor long-term prognosis. To our knowledge, such cases of retroperitoneal SC-RMS compressing the abdominal viscera and resulting in hydroureteronephrosis have never been reported before.This publication has 13 references indexed in Scilit:
- Pancreatic pleomorphic rhabdomyosarcomaInternational Journal of Surgery Case Reports, 2015
- Primary Intra-Abdominal Rhabdomyosarcoma in an Adult: an Unusual Presentation and Review of LiteratureIndian Journal of Surgical Oncology, 2015
- Spindle cell rhabdomyosarcoma of the retroperitoneum: an unusual case developed in a pregnant woman but obscured by pregnancy.2014
- Spindle Cell Rhabdomyosarcoma: A Brief Diagnostic Review and Differential DiagnosisArchives of Pathology & Laboratory Medicine, 2013
- The Management of Adult Soft Tissue SarcomasAmerican Journal of Clinical Oncology, 2009
- Comparing Adult and Pediatric Rhabdomyosarcoma in the Surveillance, Epidemiology and End Results Program, 1973 to 2005: An Analysis of 2,600 PatientsJournal of Clinical Oncology, 2009
- Pediatric rhabdomyosarcomas and nonrhabdomyosarcoma soft tissue sarcomaJournal of Indian Association of Pediatric Surgeons, 2006
- Spindle Cell Rhabdomyosarcoma in AdultsThe American Journal of Surgical Pathology, 2005
- Adult rhabdomyosarcomaCancer, 2002
- Pleomorphic Rhabdomyosarcoma in Adults: A Clinicopathologic Study of 38 Cases with Emphasis on Morphologic Variants and Recent Skeletal Muscle-Specific MarkersLaboratory Investigation, 2001