Pentalogy of Cantrell with Sternum Agenesis—A Case Report
Open Access
- 1 January 2020
- journal article
- research article
- Published by Scientific Research Publishing, Inc. in Open Journal of Thoracic Surgery
- Vol. 10 (01), 1-5
- https://doi.org/10.4236/ojts.2020.101001
Abstract
Introduction: Pentalogy of Cantrell is a rare disorder described by Cantrell in 1958 and characterized by heart anomalies, involving defects of the diaphragm, abdominal wall, supraumbilical region and pericardium. Methods: We report a case of the disease that presented with agenesis of the sternum and partial absence of costal cartilage, treated by a multi-disciplinary team. Results: The patient underwent median sternotomy. An enlarged heart, compromising the pulmonary trunk and the right ventricle, and a left superior vena cava were identified. The right atrium was opened and an interventricular communication of around 10 mm in diameter was seen through the tricuspid valve. Following the repair of the heart defects, chondroplasty and placement of biological mesh (Bioway of Gore) were performed. Conclusion: A Successful surgical treatment for Cantrell Syndrome includes correction of the cardiac malformation, a good repair of thoracoabdominal wall.Keywords
This publication has 7 references indexed in Scilit:
- Ectopia Cordis Associated with Pentalogy of Cantrell—A Case ReportRBGO Gynecology & Obstetrics, 2019
- Repair of inferior sternal cleft using a titanium plate in an infant with pentalogy of CantrellJournal of Cardiac Surgery, 2016
- One-stage surgical treatment for Cantrell syndrome without repairing the left ventricular diverticulum: a case reportCardiology in the Young, 2015
- Pentalogía de Cantrell: reporte de un caso de padres consanguíneosBiomédica, 2011
- Cantrell Syndrome. Case report of an adultArquivos Brasileiros de Cardiologia, 2000
- Cantrell’s Syndrome: A Challenge to the SurgeonThe Annals of Thoracic Surgery, 1998
- Pentalogia de Cantrell: relato de casoBrazilian Journal of Cardiovascular Surgery, 1995