Kasabach Merritt syndrome in a 28-year-old female: A strange case report
Open Access
- 11 November 2021
- journal article
- Published by Scientific Scholar in Journal of Hematology and Allied Sciences
- Vol. 1, 81-83
- https://doi.org/10.25259/jhas_22_2021
Abstract
Kasabach Merritt syndrome (KMS) is a rare disease in which a benign vascular tumor that is hemangioma grows rapidly, entraps red blood cells, platelets, and coagulation factors leading to activation of coagulation cascade resulting in life-threatening disseminated intravascular coagulation and microangiopathic hemolytic anemia. KMS affects newborns and infants. Rarely can affect older children and adults with only a few cases reported in the existing literature. Clinically patients present with large cutaneous hemangioma usually involving the extremities however visceral organs may be involved in some cases along with anemia, thrombocytopenia, coagulopathy, and bleeding. We report a case of KMS in a 28-year-old female who presented with bilateral subdural hematoma, thrombocytopenia, and consumption coagulopathy. She was given seven days course of methylprednisolone to which she responded well.Keywords
This publication has 11 references indexed in Scilit:
- Retrospective study on the outcomes of infantile tufted angioma complicated by Kasabach-Merritt PhenomenonClinica Chimica Acta; International Journal of Clinical Chemistry, 2018
- Kasabach-Merritt PhenomenonJournal of Pediatric Hematology/Oncology, 2009
- Treatment of Kasabach-Merritt syndrome: a stepwise regimen of prednisolone, dipyridamole, and interferonInternational Journal of Dermatology, 2003
- Stepwise multimodal approach in the treatment of Kasabach-Merritt syndrome.Pediatrics International, 2000
- Outcome of radiation therapy for patients with Kasabach-Merritt syndromeEndocrine, 1997
- Development of Kasabach-Merritt syndrome following needle aspiration of a hemangiomaPediatric Emergency Care, 1992
- Kasabach-Merritt syndrome in infantsJournal of the American Academy of Dermatology, 1983
- Disseminated intravascular coagulation after excision of giant hemangiomaThe American Journal of Surgery, 1974
- Hemangioma and thrombocytopeniaJournal of Pediatric Surgery, 1970
- CAPILLARY HEMANGIOMA WITH EXTENSIVE PURPURAAmerican Journal of Diseases of Children, 1940