While the involvement of the central nervous system in clinical phenotype of patients with Charcot Marie Tooth (CMT) disease has been reported in the past, the association with epilepsy has rarely been described. Only a few patients with CMT disease were reported in the literature to have epilepsy. We report the observation of a patient with CMT1A who also developed epileptic seizures. It is interesting to describe this case to show whether CMT and epilepsy are two different expressions of the same genetic abnormality or two different entities occurring together.