Adult-onset Still’s disease complicated with macrophage activation syndrome: A case report
- 23 July 2022
- journal article
- Published by Peertechz Publications Private Limited in Journal of Vaccines and Immunology
- Vol. 8 (1), 023-028
- https://doi.org/10.17352/jvi.000051
Abstract
Adult-onset Still’s disease is a rare systemic disease while macrophage activation syndrome is a fulminant complication of Still’s disease. As mortality is high in macrophage activation syndrome, prompt diagnosis is crucial to commence definitive management. Adult-onset Still’s disease is a rare systemic disease while macrophage activation syndrome is a fulminant complication of Still’s disease. As mortality is high in macrophage activation syndrome, prompt diagnosis is crucial to commence definitive management. Macrophage activation syndrome is a complication of adult-onset Still’s disease. When first-line immunosuppressives fail, second-line medications including biologic therapy can be considered with good results.Keywords
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